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COX10 Rabbit anti-Human, Mouse, Rat, Polyclonal, Proteintech

Rabbit Polyclonal Antibody

Brand:  Proteintech 10611-2-AP-150UL

Additional Details : Weight : 0.00010kg

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Product Code. 16887093

  • 3313.85 SEK / 150µL
Estimated Shipment: 06-12-2021

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Description

Description

Defects in COX10 are a cause of mitochondrial complex IV deficiency (MT-C4D); also known as cytochrome c oxidase deficiency. A disorder of the mitochondrial respiratory chain with heterogeneous clinical manifestations, ranging from isolated myopathy to severe multisystem disease affecting several tissues and organs. Features include hypertrophic cardiomyopathy, hepatomegaly and liver dysfunction, hypotonia, muscle weakness, excercise intolerance, developmental delay, delayed motor development and mental retardation. A subset of patients manifest Leigh syndrome.
Specifications

Specifications

COX10
0.33 mg/mL
PBS with 50% glycerol and 0.1% sodium azide; pH 7.3
Q12887, Q8CFY5
COX10, Heme O synthase
Rabbit
IgG
150 μL
-20°C
Primary
1352, 691853, 70383
Western Blot
Unconjugated
COX10
Liquid
Cox10
COX10 Fusion Protein Ag0930
Antigen Affinity Chromatography
RUO
Antibody
Polyclonal
Human, Mouse, Rat
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